Interstitial lung disease in dermatomyositis and polymyositis: Clinical manifestations and diagnosis - UpToDate
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Interstitial lung disease in dermatomyositis and polymyositis: Clinical manifestations and diagnosis Authors:Paul F Dellaripa, MDSonye K Danoff, MD, PhD Section Editors:Ira N Targoff, MDKevin R Flaherty, MD, MS Deputy Editors:Paul Dieffenbach, MDPhilip Seo, MD, MHS Literature review current through: Aug 2026. This topic last updated: Aug 26, 2026. INTRODUCTION Dermatomyositis (DM) and polymyositis (PM) are classified as idiopathic inflammatory myopathies. Among patients with DM or PM, interstitial lung disease (ILD) is a major cause of morbidity and mortality. A general approach to the…
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